Abstract
Sturge-Weber syndrome (SWS), sometimes referred to as encephalotrigeminal angiomatosis, is a rare congenital neurological and skin disorder. It is one of the phakomatoses which is often associated with port-wine stains of the face, glaucoma, seizures, mental retardation, and ipsilateral leptomeningeal angioma. It is characterized by proliferation of arteries of the brain, resulting in multiple angiomas that occur on the same side due to arteriovenous malformations. Normally, only one side of the head is affected and mainly results from the errors in both the mesodermal and ectodermal development. Here, we report a rare case of SWS having oral and facial manifestations, where an 8-year-old boy had actually come for treatment of swollen gums, and on examination, we found that he had typical signs and symptoms of this rare developmental anomaly. The main purpose of this publication is to make the clinician aware of the oral manifestations that are seen in the patients with SWS and also to lay stress on the importance of radiographs in the diagnosis of this syndrome.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
