Abstract
Abstract The case of an 8-year-old female affected by Noonan syndrome is presented. The orofacial findings comprised a skeletal Class III malocclusion, transverse maxillary deficiency, a long face and severe tooth size-arch length discrepancy. The interceptive orthodontic approach focused on addressing the patient’s problems while keeping treatment as simple as possible. Management consisted of rapid maxillary expansion and serial extractions in the mandible. Treatment alternatives and results are discussed and a one-year follow-up is provided.
Highlights
Noonan syndrome (NS, OMIM 163950) is a relatively common, autosomal dominant, multisystem disorder with complete penetrance and variable expressivity, mainly characterised by a typical facial pattern, short stature and heart defects.[1]
The records indicated the presence of a skeletal Class III malocclusion, a high-arched palate with a right lateral cross-bite, an anterior open bite, severe crowding in both arches, and a mandibular dental midline shifted to the right as a consequence of the premature loss of the right lower deciduous canine
A variation of a serial extraction programme often begins with the removal of the deciduous canines, which helps to resolve incisor crowding
Summary
The case of an 8-year-old female affected by Noonan syndrome is presented. The orofacial findings comprised a skeletal Class III malocclusion, transverse maxillary deficiency, a long face and severe tooth size-arch length discrepancy. The interceptive orthodontic approach focused on addressing the patient’s problems while keeping treatment as simple as possible. Management consisted of rapid maxillary expansion and serial extractions in the mandible. Treatment alternatives and results are discussed and a one-year follow-up is provided.
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