Organisation de la prise en charge des besoins transfusionnels des patients atteints d’hémoglobinopathie à l’Établissement français du sang Bretagne

Abstract

Brittany is a low prevalence region for hemoglobinopathies. Despite of that, the number of patients is increasing each year. In 2013, 140 patients were known at the EFS Bretagne, and medical consultations are growing for 50 % each year since 2011. The consequence is an increase of needs of 22 % of compatible packed red blood cells. To anticipate the announced progress, various actions were implemented as study groups, creation of a new informatic prescription for red blood cells phenotyping, promotion of donation, transfusion organisation. ResultsFifthty-nine percent of the 400 ABO RH-KELL, FY, JK, MNS 3, 4, red blood cells were realised on the basis of this new informatic prescription, as the 99 % of the packed red blood cells identified Fy (a- b-). So, 92 % of the compatible transfused packed red blood cells were already in stock when the patients needed them. ConclusionsIn Brittany, that organisation leads to assume qualitative and quantitative transfusion for sickle cell disease in more than 90 % of cases, with fast distribution. In the same time promotion of donation is done to increase the diversity of donors.