Oral Rehabilitation for Amniotic Band Syndrome: An Unusual Presentation.

Krishna Sharma,Kavita Hotwani

doi:10.5005/jp-journals-10005-1283

Krishna Sharma, Kavita Hotwani

Open Access

https://doi.org/10.5005/jp-journals-10005-1283

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Abstract

ABSTRACTAmniotic band syndrome (ABS) is a congenital disorder caused by entrapment of fetal parts in fibrous amniotic bands while in utero. The syndrome is underdiagnosed and its presentation is variable. The syndrome has been well described in the pediatric, orthopedic and obstetric literature; however, despite the discernable craniomaxillofacial involvement, ABS has not been reported in the dental literature very often. The present report describes a case of a patient with ABS and concomitant dental findings.How to cite this article: Hotwani K, Sharma K. Oral Rehabilitation for Amniotic Band Syndrome: An Unusual Presentation. Int J Clin Pediatr Dent 2015;8(1):55-57.

Highlights

Amniotic band syndrome (ABS) is a congenital disorder caused by entrapment of fetal parts in fibrous amniotic bands while in utero
We present a case of a patient with ABS and concomitant dental findings
On further medical evaluation and clinical examination, it was found that the patient had congenital deformity of phalanges of left hand with rudimentary fingers

Summary

INTRODUCTION

Amniotic band syndrome (ABS) is a congenital disorder caused by entrapment of fetal parts in fibrous amniotic bands while in utero. The rupture of the amnion has secondary effects on the fetus, which produces malformation and deformation due to interruption of normal morphogenesis. It is known as ADAM complex.[1]. The syndrome is underdiagnosed and its presentation is so variable that no two cases are exactly identical. We present a case of a patient with ABS and concomitant dental findings. It was found that the patient had multiple carious lesions and over-retained deciduous teeth. On further medical evaluation and clinical examination, it was found that the patient had congenital deformity of phalanges of left hand with rudimentary fingers. A treatment plan was formulated and the rehabilitation resulted in restoration of patient’s oral health considerably (Table 1 and Fig. 1)

DISCUSSION

Preventive