Oral findings in West syndrome – A Case Report

Sheetal Dilip Badnaware,Shely Pratik Dedhia,Adesh Kakade,Rajiv Desai

doi:10.14295/bds.2017.v20i3.1371

Sheetal Dilip Badnaware, Shely Pratik Dedhia + Show 2 more

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https://doi.org/10.14295/bds.2017.v20i3.1371

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Abstract

West syndrome is a severe form of epilepsy syndrome which is characterized by triad of infantile spasms, EEG findings (hypsarrhythmia) and developmental delay. Very few literatures is available on the dental findings and management of West syndrome. This case report presents a 8 year old male child with cryptogenic form of West syndrome having a history of multiple clusters of infantile spasms and typical dental findings. Dental treatment of the case has been discussed and preventive measures and treatment of west syndrome has been described. KeywordsWest syndrome; White spot lesion; General anesthesia.

Highlights

INTRODUCTIONA severe form of epilepsy syndrome, is a triad of infantile spasms (typical age when seizures start), hypsarrthymia and mental retardation [1]
West syndrome, a severe form of epilepsy syndrome, is a triad of infantile spasms, hypsarrthymia and mental retardation [1]
This article documents the case of an 8 year old male child diagnosed with West Syndrome with more emphasis on the orodental findings and their dental treatment

Summary

INTRODUCTION

A severe form of epilepsy syndrome, is a triad of infantile spasms (typical age when seizures start), hypsarrthymia and mental retardation [1]. Spasms usually cease by 5 years of age, but other seizure types are reported in as many as 60% of children with West syndrome even after cessation of spasms [5]. This article documents the case of an 8 year old male child diagnosed with West Syndrome with more emphasis on the orodental findings and their dental treatment. Patient was a known case of cryptogenic form of West syndrome and was diagnosed at the age of one and a half years. The intra oral examination was done and intra oral periapical radiographs (IOPA) [Figure 7] were taken under general anesthesia. 64,65,73,74,75,84,85 had carious lesions, out of which 74,75,84 and 85 had multisurface carious lesions [Figure 3 and 4] On radiographic assessment, these teeth showed root resorption.

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