Optional Method with Innovative Instrument for Ohvira Syndrome Treatment: Case Reports and Review of Literature

Abstract

OHVIRA syndrome is a rare condition usually present during early puberty, after menarche. The main symptoms are caused by the obstruction of hemivagina and accumulation of blood, which cause the symptoms such as dysmenorrhea, chronic pelvic pain or pelvic mass. Transvaginal septectomy is the best way to treat of patient’s obstructive hemivagina. However, in young patients, the small vagina canal is a significant limitation, and it is challenging to explore the surgical field. Due to the uncommon condition at young ages and variation in coexisting anomalies, approach techniques and instruments are still under development. In this case series, we present 2 cases of OHVIRA syndrome who received surgical treatment at Ramathibodi Hospital, Mahidol University. Both cases used the same innovative vaginal retractor, designed and modified for the young patient with OHVIRA syndrome. After the procedure, patients showed no complications or recurrence up to 2 years of follow-up.