Abstract

Background and aim: A relatively common sex- linked dermatitis characterized by a congenital dysplasia of one or more ectodermal structures is Ectodermal dysplasia (ED). Common signs include fragile skin and nails, defective teeth and salivary glands, frontal bossing with prominent supra orbital ridges, nasal bridge depression and protuberant lips. There are often a few conical teeth existing (hypodontia or Oligodontia) that results in generalized spacing. Deciduous and/or the permanent dentition may fail to form (anodontia), and, consequently, hypoplasia of jaws may happen in both cases. This article reports a case of ED and shows how to handle it. Case report: A 5 years old girl with HED visited SBMU, school of dentistry. Clinical examination showed hypotrichosis following the missing of eyelashes and eyebrows, dry skin, saddle nose and pigmentation on the legs which are characteristics of ED. Partial denture for lower jaw and composite restoration for upper jaw was used as the treatment plan. Conclusion: Preventive treatments are very crucial to save present teeth in ED patients. One treatment option is to use removable dentures as a cost-benefit and desired intermediate treatment to restore both function and esthetics and improve patient’s psychological status in Oligodontia cases.

Highlights

  • Ectodermal dysplasia (ED) is commonly known as a rare inherited disorder characterized by defective development ofA 5-year-old girl visited the school of Dentistry, Shahid Beheshti University of medical Sciences with chief complaint of missing teeth

  • Thin and underdeveloped residual ridge is presented in these groups which are covered by a thin layer of mucosa topped by a cord of movable connective tissue [5]

  • To initiate the treatment by a removable that is found to be more tolerable for children when at a school age [11]

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Summary

Introduction

Ectodermal dysplasia (ED) is commonly known as a rare inherited disorder characterized by defective development ofA 5-year-old girl visited the school of Dentistry, Shahid Beheshti University of medical Sciences with chief complaint of missing teeth. While mastication was a problem, but the main complaint of the patient was about esthetic problems since it is a more important factor for girls than boys. The treatment plan was set as to do an overdenture for mandibular and composite reshaping for maxillary teeth. The results of follow ups were again as the previous case, first the acceptance was good since esthetic and function of the kid’s teeth were improved but followed by a limited use of the denture due to unsatisfactory motivation and control of parents.

Results
Conclusion

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