Abstract
Observation: We present a case of a 21-year-old Pakistani female with hypoplastic amelogenesis imperfecta (AI), microdontia, and multiple gingival swellings overlying impacted teeth. The gingival swellings were diagnosed as AI-associated odontogenic fibroma (OF)-like lesions on histology. Commentary: AI is an inherited enamel defect that may present in association with microdontia, root abnormalities, taurodontism, pulp stones, gingival hyperplasia, and rarely, gingival tumors. These gingival tumors share histologic features with odontogenic fibroma (OF), a benign odontogenic neoplasm, and are referred to as AI-associated OF-like lesions in the literature. Conclusion: AI-associated OF-like lesions are rare, this case will inform oral surgeons and other dental practitioners about this process and its management.
Highlights
A 21-year-old Pakistani female was seen at the out-patient department at Riphah International University, Islamabad, with a complaint of unerupted teeth and swellings on the mandibular gingiva
The case was diagnosed as Amelogenesis imperfecta (AI) associated odontogenic fibroma (OF)-like lesions
While OF-like lesion appears to be more popular term, some authors have favored the term dental follicular hamartomas for similar presentations. This includes a case of a 10-year-old black, male patient with enamel dysplasia, delayed eruption, malformed roots, pulpal calcifications, hypercementosis, generalized gingival hyperplasia with dystrophic calcifications and pericoronal follicular hamartomas
Summary
Odontogenic fibroma-like lesions associated with amelogenesis imperfecta: short case. While most OF-lesion are pericoronal, there are two reports of central occurrences This includes a case of rough hypoplastic type AI with multiple OF-like lesions causing displacement of impacted teeth, anterior open bite, pulpal calcifications, hypercementosis and generalized gingival overgrowths. While OF-like lesion appears to be more popular term, some authors have favored the term dental follicular hamartomas for similar presentations This includes a case of a 10-year-old black, male patient with enamel dysplasia, delayed eruption, malformed roots, pulpal calcifications, hypercementosis, generalized gingival hyperplasia with dystrophic calcifications and pericoronal follicular hamartomas. O’Connell S used it for his report of a 7-year-old female with AI, dental follicular hamartomas, generalized gingival overgrowth, anterior open bite, multiple impactions and dilacerated roots [5]
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