Abstract

Servicio de Dermatologia, Instituto Valenciano de Oncologia, Valencia, Spain the diagnosis of membranous aplasia cutis congenita (ACC) of the scalp with hair collar sign, associated with polydactyly and syndactyly. This diagnosis could correspond to ACC group 1 of the scalp with no associated abnormalities or associated with isolated anomalies.3 Two aspects should be mentioned in relation to this case. First of all, a comprehensive assessment should be performed on any congenital lesion of the midline before surgical excision or biopsy. Computed tomography is the most accurate method for assessing cranial defects. Any bone defect observed with this method should be examined by magnetic resonance imaging to determine if there is transcranial extension of soft tissue. If there is no cranial defect and the lesion is consistent with membranous aplasia cutis, then biopsy is not necessary. Secondly, the association of various cutaneous markers on the scalp, such as the hair collar sign and vascular malformations, increases the possibility of associated cervical dysraphism.4,5

Full Text
Published version (Free)

Talk to us

Join us for a 30 min session where you can share your feedback and ask us any queries you have

Schedule a call