Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single septate uterus: first case report

Abstract

ObjectiveTo describe an unusual case of an Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome with a single septate uterus.DesignCase report.Materials and methodsCase review and review of literature.ResultsConclusionsCases of a single septate uterus with two cervices are rare. The OHVIRA Syndrome has been reported and described as an obstructed hemivagina and ipsilateral renal anomaly. This Syndrome is associated with a double or bicornuate uterus and has two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a not previously described congenital anomaly of the female reproductive tract which is a variant of the OHVIRA Syndrome: the OHVIRA Syndrome with a single septate uterus. From a fertility standpoint, cases of a single septate uterus with two cervices are managed differently than two uteri with two cervices. This is the first case report of a single uterus with two uterine cavities, two cervices and an obstructed hemivagina with ipsilateral renal agenesis. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant. ObjectiveTo describe an unusual case of an Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome with a single septate uterus. To describe an unusual case of an Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome with a single septate uterus. DesignCase report. Case report. Materials and methodsCase review and review of literature. Case review and review of literature. Results ConclusionsCases of a single septate uterus with two cervices are rare. The OHVIRA Syndrome has been reported and described as an obstructed hemivagina and ipsilateral renal anomaly. This Syndrome is associated with a double or bicornuate uterus and has two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a not previously described congenital anomaly of the female reproductive tract which is a variant of the OHVIRA Syndrome: the OHVIRA Syndrome with a single septate uterus. From a fertility standpoint, cases of a single septate uterus with two cervices are managed differently than two uteri with two cervices. This is the first case report of a single uterus with two uterine cavities, two cervices and an obstructed hemivagina with ipsilateral renal agenesis. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant. Cases of a single septate uterus with two cervices are rare. The OHVIRA Syndrome has been reported and described as an obstructed hemivagina and ipsilateral renal anomaly. This Syndrome is associated with a double or bicornuate uterus and has two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a not previously described congenital anomaly of the female reproductive tract which is a variant of the OHVIRA Syndrome: the OHVIRA Syndrome with a single septate uterus. From a fertility standpoint, cases of a single septate uterus with two cervices are managed differently than two uteri with two cervices. This is the first case report of a single uterus with two uterine cavities, two cervices and an obstructed hemivagina with ipsilateral renal agenesis. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.