Novel approach to resection of an obstructing longitudinal septum with a microperforation and absent hematocolpos

Abstract

Background: Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) is a rare urogenital tract malformation characterized by uterus didelphys, obstructed hemivagina and renal agenesis. Patients often present after menarche with cyclic dysmenorrhea and hematocolpos. Treatment is surgical resection of the obstructing septum. When microperforation of the longitudinal septum is present, the clinical picture can be more insidious. In addition, complete and safe surgical resection of the poorly delineated septal cavity is challenging.