Non syndromic unilateral posterior lenticonus

Abstract

An 18 year-old girl presented with complaints of difficult in seeing distant objects with her left eye since childhood. On ocular examination: uncorrected visual acuity was determined by counting fingers 4 m for left eye, and 10/10 for the right eye. And the best-corrected visual acuity for distance in left eye was 1/10. On slit lamp examination, anterior segment was normal in the left eye except for a posterior protrusion of the lens capsule associated with posterior subcapsular and cortical cataract in the central area (A,B), and oil droplet reflex was seen in retroillumination (C). Anterior segment examination of the right eye was normal, and posterior segment examination was normal in both eyes. There was no ocular or systemic abnormality or family history associated. Our diagnosis was non-syndromic unilateral posterior lenticonus. The first clinical description of lenticonus was in 1888 by Meye. it is a localized bulging of the lens capsule and the underlying cortex of the anterior or, more commonly, the posterior lens capsule. The diagnosis is essentially clinical, which is made by biomicroscopic examination. Posterior lenticonus may be associated with other abnormalities, such as Lowe oculocerebral syndrome, but it occurs usually sporadically in approximately 1-4 of every 100,000 children and is mostly unilateral in 8-10% cases.