Neurofibromatosis Type I Plexiform Geante of the Buttock in a Surgical Setting in a Second Referral Hospital

Abstract

Neurofibromatosis type I (NFI) or Von Reccklinghausen disease is a rare pathology in the surgical setting. We report the observation of a giant plexiform neurofibromatosis type I (NFI) of the buttock in a 61-year-old patient. The pathology was responsible for functional discomfort, unaesthetic and a problem of personal hygiene (after the stool). The she, unaesthetic and a problem of body hygiene (after the stools). The diagnosis of neurofibromatosis was confirmed according to the diagnostic criteria of the National Institue of Health (NIH) consensus conference. Surgical excision was performed, the anatomo-pathological examination of the surgical specimen was a benign tumor, the long-term evolution was satisfactory without local recurrence and a resumption of the activities of daily life.