Neonate in Respiratory Distress with To-and-Fro Shunt from Aorta to Right Ventricle

Abstract

A cyanotic newborn in heart failure on diagnostic transthoracic echocardiography revealed pulmonary atresia with intact ventricular septum with a vertical patent ductus arteriosus supplying from the underside of arch of aorta. There was an anomalous origin of right coronary artery from the left coronary artery. It was also associated with a coronary cameral fistula with a continuous to-and-fro shunt from the aorta through the dilated coronary to the right ventricle with a bidirectional shunt. We intend to report this case because because pulmonary atresia with single coronary artery with coronary cameral fistula is uncommon and are sparsely reported, and sparsely reported, and and are best managed by univenventricular repair followed by cardiac transplanatation.