Necrotizing autoimmune myopathy: an emerging entity in the spectrum of inflammatory myopathies

Abstract

Background: Necrotizing autoimmune myopathy is a relatively newly recognized rare form of idiopathic inflammatory myopathy. It presents clinically with symmetrical proximal muscle pain and weakness, associated with a markedly elevated Creatine kinase level. These myopathies are usually immune mediated with a good response to immunotherapy. Case presentation: We present a case of a 32 year old man of Asian descent, having a 6 months history of symmetrical proximal muscle weakness. Patient underwent extensive workup and was diagnosed with Necrotizing autoimmune myopathy. Conclusion: The disease process of Necrotizing autoimmune myopathy is still not completely understood. However, a delay in the diagnosis may lead to potential complications as the disease progresses rapidly.