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Abstract
Congenital midline swellings of nose are encountered rarely, and nasal gliomas constitute about 5% of such lesions. Various theories have been suggested to explain the pathogenesis. Imaging preferably by MRI is mandated to study the extent and to rule out intracranial extension. Clinically, these masses are firm and incompressible. Histologically, they are made up of astrocytes and neuroglial cells, embedded in fibrous and vascular connective tissue. The mainstay of treatment is conservative surgical excision because nasal gliomas are slow-growing, rarely recurrent, and have no malignant potential. We present a case of congenital extranasal glioma with psammomatous calcification and without any intracranial extension in an eighteen month old boy. -------------------------------------------- Cite this article as : Sherwani RK, Akhtar K, Ray PS, Ahmad SS. Nasal glioma with psammomatous calcification- An unusual presentation. Int J Cancer Ther Oncol 2014; 2(2):02027. DOI: 10.14319/ijcto.0202.7
Highlights
The developmental anomalies of the nose encompass a diverse group of conditions, which include nasal dermoids, gliomas, encephaloceles, nasal clefts, proboscis lateralis, polyrrhinia, nasopharyngeal teratoma, and epignathus.[1]
Nasal gliomas are one form of the congenital midline nasal masses that usually present at birth
We report a case of extranasal glioma with psammomatous calcifications in eighteen months old boy
Summary
The developmental anomalies of the nose encompass a diverse group of conditions, which include nasal dermoids, gliomas, encephaloceles, nasal clefts, proboscis lateralis, polyrrhinia, nasopharyngeal teratoma, and epignathus.[1]. Nasal gliomas are one form of the congenital midline nasal masses that usually present at birth They are rare, benign, congenital tumours, which arise from abnormal embryonic development. They are nonencapsulated CNS masses of neurogenic origin, which have lost their intracranial connections, and present as an obvious external or intranasal mass at birth, without associated surgical symptoms.[2, 3] The term "nasal glioma" is a confusing misnomer as it implies a neoplastic condition with malignant potential, which it is not. The boy had a 3 × 3 cm superficial purple, soft to firm mass with a smooth surface over his nasal bridge. Magnetic resonance imaging (MRI) of the brain showed a well-defined soft tissue attenuation lesion, at the root of the nose without any underlying bony defect or intracranial extension, measuring 2.9 × 2.9 × 2.5 cm. (Figure 1)The lesion showed mild heterogenous enhancement with evidence of concentric calcifications within the lesion
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