下部脳神経麻痺を初発としたハント症候群

Abstract

We report a case of Hunt syndrome with the primary complaint of lower cranial nerve paralysis. The patient experienced not only lower cranial nerve paralysis, but also, finally, paralysis of the facial nerve. The patient was a 68-year-old woman. She came to the hospital complaining of herpetic vesicles around the right ear and pain, vertigo, and hoarseness, but there was no facial palsy. Hydrocortisore sodium succinate and acyclovir were administered intravenously.Twelve days after, she developed right facial palsy. Prednisolone and Valaciclovir hydrochloride were orally administered. Fifty Four days after disease onset, the function of all cranial nerves recovered completely.A review of the Japanese literature revealed 44 cases of Hunt syndrome with multiple cranial nerve palarisis from 1954-2005. In our case, the development of right facial palsy occurred later than all other symptoms. The late-onset facial palsy was only 5 cases and rare.