Multiple Trichoepitheliomas in the Lines of Blaschko

Abstract

We report a unique occurrence of linear multiple trichoepitheliomas that follow Blaschko lines on the face of an otherwise healthy 8-year-old African American girl. Per the mother, the lesions had been present since birth. The diagnosis was made based on the histologic presence of palisading basaloid cells surrounding central areas of follicular differentiation and papillary mesenchymal bodies. To the authors' best knowledge, this is the first report of linear multiple trichoepitheliomas following the lines of embryologic cutaneous cell development, and possibly, the first of congenital multiple trichoepitheliomas.