Multilocular Cystic Nephroma: A Rare Presentation in a Young Female

Abstract

Multilocular cystic nephroma represents a rare benign cystic lesion of the kidney, which usually presents as a unilateral multicystic renal mass without solid elements. It has a bimodal distribution presenting in children between three months to two years, and over 30 years of age in adults. Only 5% of cases occur in young adults. We report case of a 16-year-old female who came with complaints of dull non-radiating pain in left flank since three months and hematuria since 1 week. On palpation, a mass was felt in left subcostal and lumbar region. Ultrasonography and Computed tomography scan showed multiloculated cystic mass in left kidney. Left side nephrectomy was done and specimen was sent for histopathology. Based on histopathological findings, an impression of multilocular cystic nephroma was given. Multilocular cystic nephroma should be considered in the differential diagnosis of malignant cystic renal tumors in both children and adults. Its nonspecific clinical presentations and confusing radiological features create difficult preoperative differentiation. Better diagnostic methods in future may spare the kidney.