“Mixed” gonadal dysgenesis with gonadoblastoma in situ

Abstract

T H E T E R M “mixed’ gonadal dysgenesis refers, according to Sohval,14 to the coexistence of a rudimentary, fibrous “streak” gonad on one side and a testis on the other. Bergada and associates1 named this condition asymmetrical gonadal differentiation. Such gonads are situated abdominally in the normal position of ovaries. Uterus and Fallopian tubes are present, but usually they are underdeveloped or rudimentary. Several such cases have been reported in the literature,lm4 but were not classified as “mixed gonadal dysgenesis,” which seems to be most appropriate.