Mixed cystic lymphatic malformations

Abstract

Introduction: Cystic lymphatic malformations (CLM) are rare benign, slow-flowing congenital malformations composed of abnormal cystic dilatations. They can be microcystic, macrocystic or very rarely mixed. We describe a rare case of mixed CLM in a 12-year-old female patient. Observation: A 13-year-old girl, from a consanguineous marriage, who presented to our structure for a swelling of the right forearm which appeared 3 weeks previously and which was progressively increasing in size. Examination found a soft, depressible and painful subcutaneous mass in the right forearm associated with vesicular hemorrhagic lesions grouped into plaques in the ipsilateral arm initially treated as shingles without improvement. Diagnosis of mixed CLK was made clinically and confirmed on imaging. Therapeutic abstention was recommended with monitoring and local treatment. Discussion: The originality of our observation lies in the association of micro and macrocystic CLM, the late appearance of the lymphatic malformation, and clinical presentation of lymphangiectasias confused with shingles. Key words: Mixed lymphatic malformations, MLK, Vascular malformations