Abstract

BackgroundThis study was undertaken to determine the midterm outcome in patients with anomalous left coronary artery from the pulmonary artery (ALCAPA) undergoing coronary reimplantation and Takeuchi repair.MethodsA retrospective review of patients who had ALCAPA repair between January 2009 and December 2015. Mortality, echocardiography assessment of left ventricular function including ejection fractionand, shortening fraction, severity of mitral regurgitation, stenosis of the coronary ostium were studied retrospectively.ResultsSixteen patients were described. The mean age at the time of surgery was 22.5 ± 10.3 years (range, 9 months-35.6 years) and 2 patients were younger than 1 year old, Surgical interventions included left coronary artery reimplantation in 13 patients (81 %) and Takeuchi repair in 3 (19 %). Concomitant mitral valve repair was performed in 2 cases, no cases required mechanical circulatory support postoperatively. There was no mortality. At median follow-up of 4.6 years, EF improved from 33.2 % ±6.8 % to 60.9 % ± 8.1 % (p <0.05), mean SF from 28.5 % ± 12.1 % to 40.2 % ± 5.4 % (p <0.05). Only one patient was with moderate mitral regurgitation. All 16 cases had normal ejection fraction and shortening fraction without stenosis of the coronary ostium at last follow-up.ConclusionsEarly establishment of a 2-coronary artery achieved excellent outcomes without morbidity and mechanical circulatory support. Normal ejection fraction and shortening fraction recovered smoothly. There is no stenosis of the coronary ostium at the midterm follow-up.

Highlights

  • This study was undertaken to determine the midterm outcome in patients with anomalous left coronary artery from the pulmonary artery (ALCAPA) undergoing coronary reimplantation and Takeuchi repair

  • There is no stenosis of the coronary ostium at the midterm follow-up

  • Cardiovascular complications at follow-up occurred in 2 patients (%), Right bundle branch block in 1 patient (9 %) and the other who accepted Takeuchi repair was with mild supravalvular pulmonary stenosis which requires further follow-up

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Summary

Introduction

This study was undertaken to determine the midterm outcome in patients with anomalous left coronary artery from the pulmonary artery (ALCAPA) undergoing coronary reimplantation and Takeuchi repair. Anomalous left coronary artery from the pulmonary artery (ALCAPA), known as Bland-White-Garland syndrome, is a rare congenital abnormality that affects 1 of every 300,000 live births and accounts for 0.25 %– 0.5 % of all congenital heart defects [1, 2]. About 90 % of patients of infant type die within the 1st year of life [3]. We present 16 patients with ALCAPA and discuss the midterm outcome in patients with ALCAPA undergoing a primary LCA reimplantation and Takeuchi repair

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