Micronutrient in hyperphenylalaninemia.

Vanesa Crujeiras,María L Couce,Jaume Dalmau,Fernando Andrade,Isidro Vitoria,Ana Fermandez-Marmiesse,Rosaura Leis,Luís Aldámiz-Echevarría,Iria Roca

doi:10.1016/j.dib.2015.07.026

Abstract

The data presented here are the biochemical parameters of 156 patients with hyperphenylalaninemia. PKU patients, who, in order to maintain optimal serum Phe concentrations, receive dietary treatment consisting of a diet low in natural protein supplemented with special low protein foods and a Phe-free amino acid mixture, vitamins and minerals. The obtained data reflects a high percentage of patients with prealbumin and selenium deficiencies, as well as an increased level of folic acid. This data article is related to the research article entitled, “Vitamin and mineral status in patients with hyperphenylalaninemia”, by Crujeiras et al. [1].

Highlights

Isidro Vitoria c, Fernando Andrade b, Iria Roca d, Rosaura Leis a, Ana Fermandez-Marmiesse e, María L
The data presented here are the biochemical parameters of 156 patients with hyperphenylalaninemia
PKU patients, who, in order to maintain optimal serum Phe concentrations, receive dietary treatment consisting of a diet low in natural protein supplemented with special low protein foods and a Phe-free amino acid mixture, vitamins and minerals

Summary

Micronutrient in hyperphenylalaninemia

Vanesa Crujeiras a, Luís Aldámiz-Echevarría b, Jaume Dalmau c, Isidro Vitoria c, Fernando Andrade b, Iria Roca d, Rosaura Leis a, Ana Fermandez-Marmiesse e, María L. Unit of Gastroenterology and Nutrition, Department of Pediatrics, Hospital Clinico Universitario de Santiago, Travesía da Choupana s/n, 15706 Santiago de Compostela, A Coruña, Spain b. Unit of Metabolism, Department of Pediatrics, Hospital de Cruces, Group of Metabolism, Biocruces Health. Research Institute, CIBERER, Plaza de Cruces s/n, 48903 Barakaldo, Vizcaya, Spain c. Unit of Metabolopathies, Hospital Universitario la Fe, Bulevarsur s/n, 46021 Valencia, Spain d. Unit of Diagnosis and Treatment of Congenital Metabolic Diseases, S. Neonatology, Department of Pediatrics, Hospital Clinico Universitario de Santiago, Travesía da Choupana s/n, 15706 Santiago de Compostela, A. Hospital Clinico Universitario de Santiago, CIBERER, Health Research Institute of Santiago de Compostela (IDIS), Travesía da Choupana s/n, 15706 Santiago de Compostela, A Coruña, Spain article in foabstract

Received in revised form

Value of the data

Findings

Phe median mM