Microcystic congenital pulmonary airway malformation of the lung causing non immune hydrops fetalis and Mirror syndrome: a case report

Abstract

Congenital Pulmonary Airway Malformation (CPAM) is a rare lung anomaly with a highly variable prognosis depending on the presence of fetal hydrops and the size of the cyst. CPAM associated with fetal hydrops carries a grave fetal prognosis and development of “mirror syndrome” calls for immediate delivery of fetus as this condition is potentially life threatening for the mother, if no intervention is done. We report on the pathological findings of a non-immune hydropic fetus with cardiac shift to right side, moderate hydromnios and a rare maternal condition which “mirrors” the sick fetus known as “mirror syndrome” by developing edema and high blood pressure due to microcystic CPAM at 26 weeks of gestation.