Melorheostosis of the Left Upper Limp

Bahri Evren,Ahmet Sigirci,Ersoy Kekilli,Ayse Cikim Sertkaya,Ismail Koksal

doi:10.4236/ojmi.2012.23020

Abstract

Melorheostosis, also known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, skle-rosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowing down a candle”. We report on a 43-year-old woman with melorheostosis who had pain in the upper limp for 10 years, limitation of joint movement and a deformity in the left third finger. Radiographies and bone scintigraphy were evaluated. All lesions of melorheostosis in radiography were seen in bone scintigraphy. More than half of increased uptakes on bone scintigra-phy are due to degenerative process.

Highlights

Melorheostosis, known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, sklerosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowing down a candle”
We report on a 43-year-old woman with melorheostosis who had pain in the upper limp for 10 years, limitation of joint movement and a deformity in the left third finger
More than half of increased uptakes of hands on bone scintigraphy are due to degenerative process

Summary

Introduction

Melorheostosis, known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, sklerosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowing down a candle” [1,2]. All bones may be affected, especially those of the lower limb. This disease is rather unusual, and only a few cases have been reported in the humerus [4,5,6,7,8,9,10], and in the forearm and hand [37,11,12]. Lesion localization is very important in the prevention of fracture, treatment and follow-up. Beside bone scintigraphy can easy detect of suspicious lesions in whole body, it can enables the detection of metabolically active lesions which is important the choice of treatment options, patient monitoring and the detection of lesions that cause clinical complaints [12]

Case Report

Discussion