Melanotic neuroectodermal tumor of infancy—A report of two cases

Abstract

The melanotic neuroectodermal tumor of infancy (MNTI) is a rare childhood neoplasm with a classical clinical presentation. It appears as a rapidly enlarging pigmented mass in the upper jaw and can be easily mistaken for a malignant neoplasm. Although possessing an aggressive growth rate and radiographic appearance, the MNTI almost always behaves in a benign fashion and can be treated with local excision. However, few cases of malignant transformation and recurrences have been reported in literature and that makes follow-up very important. This paper describes two cases of MNTI with classical histological presentation.