Massive leiomyosarcoma of the chest wall in a young child

Abstract

An unusual instance of a very large primary leimyosarcoma of the chest wall is presented. It was asymptomatic but a swelling had been noted between the left clavicle and nipple by the parents. Chest x-ray showed a massive tumor with mediastinal involvement. Preliminary biopsy indicated a leiomyosarcoma. Wide an bloc excision of the chest wall was done, including much of the 1, 2, and 3 ribs and a piece of lung. The defect was closed with Marlex mesh and covered with a U-shaped flap of pectoralis major muscle and skin. There were 4000 rads of radiotherapy plus 15 mo of chemotherapy added. To date, she remains clinically well and apparently tumor-free.