Mandibular Reconstruction in Cervical Desmoid Tumors

Ayoub Boutahar,Youssef Bouabdallah,Imane Oualili,Abdelhalim Mahmoudi,Khalid Khattala

doi:10.4236/ojped.2021.113037

Abstract

Introduction: Desmoid tumors are benign soft tissue tumors, but their infiltration character is responsible for big morbidity, especially in the cervicofacial location. Their management, therefore, represents a real challenge. Clinical case: Reporting a case of a 4-year-old girl presenting a desmoid tumor at the expense of the mandibular corpus and the right ascending ramus, with loco-regional infiltration, and whose treatment consisted of surgical resection of the tumor with Hemi-mandibulectomy and reconstruction according to the Masquelet technique. Conclusion: The traditional treatment consists of a large local excision with negative surgical margins. Head and neck fibromatosis, while rare, present a complex problem as they are often aggressive, and invade local bone, nerve and muscles, and can leave patients with a cosmetic deformity. In our case, it was a mandibular reconstruction after a large resection of a desmoid tumor with a location on the head and neck. With good consolidation, absence of recurrence, and without aesthetic sequelae at the control.

Highlights

Desmoid tumors are benign soft tissue tumors, but their infiltration character is responsible for big morbidity, especially in the cervicofacial location
Clinical case: Reporting a case of a 4-year-old girl presenting a desmoid tumor at the expense of the mandibular corpus and the right ascending ramus, with loco-regional infiltration, and whose treatment consisted of surgical resection of the tumor with Hemi-mandibulectomy and reconstruction according to the Masquelet technique
While rare, present a complex problem as they are often aggressive, and invade local bone, nerve and muscles, and can leave patients with a cosmetic deformity. It was a mandibular reconstruction after a large resection of a desmoid tumor with a location on the head and neck

Summary

Introduction

Aggressive fibromatosis, are soft tissue tumors [1]. 10% to 25% of extra-abdominal desmoid tumors develop in the head and neck region. The neck is the most common site of occurrence, followed by the face, oral cavity, scalp, and paranasal sinus [4]. In children, it typically presents as a painless, firm, possibly rapidly enlarging mass, fixed to underlying bone and soft tissue. The management of cervico-facial locations represents a real challenge When this lesion occurs in the head and neck, the proximity of vital structures and the complexity of fascial planes often preclude complete resection. We describe the contribution of the Masquelet induced-membrane technique, allowing the reconstruction of bone substance losses in large resections necessary for surgery

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Discussion

Boutahar et al DOI

Conclusion

Findings

Conflicts of Interest