Abstract
Sickle syndrome is a rare autosomal recessive disorder with incidence of live born cases It is characterized by proportionate dwarfism delayed mental development microcephaly and typical bird like facial appearance hence also called as Bird headed dwarfism Characteristic skeletal anomalies include premature closure of the cranial sutures and fifth finger clinodactyly Mental deficiency is present in half of the cases with levels of IQ below Head circumference is the most retarded parameter The cerebellum is small with a simple primitive convolutional pattern Orodental findings include retrognathia hypodontia enamel hypoplasia crowding cleft palate and Class II malocclusion This case report highlights the various clinical features and management in a pediatric patient with Sickle syndrome
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