Abstract
Management of Primary Pulmonary Synovial Sarcoma: A Case Report from Northern Pakistan and Review of Literature
Highlights
Primary pulmonary synovial sarcoma (PPSS) is an extremely unusual malignancy associated with aggressive behavior and poor clinical outcome [1]
Synovial sarcomas make up to 8% of soft tissue sarcomas most commonly seen in extremities [1]
Thoracic primary synovial sarcomas are very rare neoplasms mostly originating from lung, heart, mediastinum and esophagus [1]
Summary
Primary pulmonary synovial sarcoma (PPSS) is an extremely unusual malignancy associated with aggressive behavior and poor clinical outcome [1]. Our patient was 40-year-old female who presented with cough associated with hemoptysis She was diagnosed with Stage IV PPSE and received palliative chemotherapy. A 40-year-old female patient, non-smoker and non-addict, known diabetic and hypertensive controlled on oral medication She was investigated, and CT scan chest and abdomen was done that showed bilateral innumerable nodular opacities both intrapulmonary as well as pleura based, of variable sizes (Figure 1). CT scan repeated showed a large pleura based heterogeneously enhancing soft tissue density mass lesion along right para-vertebral region extending superiorly from T6 vertebral body to T9-10 intervertebral disc level inferiorly, adjacent to superior segment of right lower lobe measuring 71 x 61mm associated with loculated pleural effusion tracking in to right oblique fissure with associated fissural thickening (Figure 4). Patient was counseled thoroughly about the advanced nature of the disease and poor prognosis and was planned for second line chemotherapy
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