Management of a Rare Pathology in Children it is Lipomyelomenengocele about Casis Report

Bouchenaki F,Habchi N,Boustil K,Benachou S,Bakhti S

doi:10.31579/2578-8868/222

Abstract

The lipomyelomeningocele (LMMC) is a type of congenital occult spinal dysraphism consistent with the presence of lipomatous tissue adhering to the epinetic marrow, which falls through a defect of the vertical colon with the former meninges and the marrow under posture the skin. LMMC is the cause of the most frequent congenital attache between the cadre of the syndrome of the attached cord and causes a neurological deterioration due to the compression of the medical bone and the root system which is superadded. It is therefore about a girl from 6 years ago with a swelling located in the region of Lombardy after the birth of the size of a tangerine which has increased the size gradually with age. He presented the interrogation of the signs of urinary incontinence and the fact that he confirmed that he left us to fellow therapists who sent him to us for support. The local examination of the lumbosacral region revealed a single mass without other distinctive skin signs, spherical in shape, 12 × 10 cm, soft and fixed in consistency. A medullary MRI with effect, which reveals a mass of lipomate consistency at the level of lumbosacral associated with a bone spina extending from L5 to S2. Surgical treatment was indicated as the patient had urinary problems. There were no postoperative complications and after a few months postoperative symptoms improved.

Highlights

Lipomyelomeningocele (LMMC) is a type of congenital occult spinal dysraphia consisting of the presence of lipomatous tissue attached to the spinal cord, which protrudes through a defect in the spine and meninges and spinal cord to form a posterior swelling under the skin which increases in size with age
The neural ectoderm separates from the cutaneous ectoderm and the periaxial mesoderm enters intact with the unfused ventral neural ectoderm
The pathogenesis of clinical ADS syndrome is believed to arise from traction on the lower end of the spinal cord by a thick terminal filum

Summary

Introduction

Lipomyelomeningocele (LMMC) is a type of congenital occult spinal dysraphia consisting of the presence of lipomatous tissue attached to the spinal cord, which protrudes through a defect in the spine and meninges and spinal cord to form a posterior swelling under the skin which increases in size with age. A 6-year-old male patient weighing 25 kg presented with a lipoma in the lumbosacral region which gradually increased in size from birth. According to the laboratory results, the blood count remains within normal limits and the ECB in the urine showed a confirmed infection which we treated beforehand He presented on the ultrasound of the urinary tract a dilation of the pyelocaliciel tracts already testifying to the repercussions of these disorders on the upper apparatus. The patient has already performed a medullary MRI of the lumbosacral spine which revealed a mass of fat density at the lumbosacral level adhering to the dorsal surface and involving the cone which connected through a bone defect located at the level of the sacred region from L5 to S2.

Discussion

Conclusion

Oakes W