MANAGEMENT OF A DELAYED PRESENTATION OF CONGENITAL KNEE DISLOCATION IN A 14 MONTH OLD CHILD WITH LARSENS SYNDROME AND PIERRE ROBIN SEQUENCE

Abstract

Larsens syndrome is a rare genetic disorder characterized by multiple joint dislocations, abnormal facial features, and ligamentous laxity.Dislocation can involve Hips, knees, elbows, and other joints. it was first described by Larsen et al in 1950 [1]. Pierre Robin sequence is another rare congenital birth defect That is characterized by microganthia, glossoptosis and cleft palate which can lead to variety of functional abnormalities including feeding , breathing and hearing [2,3]. Here is a case report of a14-month-old child with Larsens syndrome who presented late with multiple joints dislocation including (elbow, hips, knees, and ankle), and failed management of knee dislocation.