Abstract
Malignant triton tumor (MTT) is a rare variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. We report the case of a 54-year-old male without a history of neurofibromatosis type 1 (NF1) who had a growing abdominal wall tumor diagnosed as MTT. Computed tomography (CT), magnetic resonance imaging (MRI) and 2-[F-18]-fluoro-2-deoxy-D-glucose positron emission tomography/CT (FDG-PET/CT) were performed. The MRI and FDG-PET/CT indicated that the lateral component of the tumor was composed of many proliferative cells, corresponding to the histopathological finding of a cellular proliferation of spindle-shaped cells. In light of this case and previous reports, it is apparent that FDG-PET/CT is a helpful tool for distinguishing MTT from benign peripheral nerve sheath tumor.
Highlights
Malignant triton tumor (MTT) is a variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation
FDG-positron emission tomography (FDGPET) findings of MTT have been demonstrated in only three reports [3,4,5], to the best of our knowledge
We present the case of a patient who was found to have an MTT arising in the abdominal wall, and we report the imaging findings obtained by Computed tomography (CT), magnetic resonance imaging (MRI), and FDG-PET/CT
Summary
Malignant triton tumor (MTT) is a variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. It is a rare tumor constituting 5% of all MPNSTs [1], and about two-thirds of MTT arise in patients with neurofibromatosis type 1 (NF1) [2]. Several studies reported that FDG-PET was a sensitive and specific tool for distinguishing MPNST from benign peripheral nerve sheath tumor [5,6,7,8,9,10], there has been very little discussion about the details of the radiological features of MTTs. We present the case of a patient who was found to have an MTT arising in the abdominal wall, and we report the imaging findings obtained by CT, MRI, and FDG-PET/CT
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Free) 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call
