Malignant paraganglioma of the mesentery A case report and review of literature

Michael Chetrit,Lucas Sideris,Pierre Dube,Guy Leblanc,Virginie Royal

doi:10.1186/preaccept-1456281118627023

Michael Chetrit, Lucas Sideris + Show 3 more

Open Access

https://doi.org/10.1186/preaccept-1456281118627023

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Abstract

Malignant paraganglioma of the mesentery A case report and review of literature

Highlights

With an annual incidence estimated at 1/100,000, paragangliomas represent ten percent of catecholamine secreting tumors
Some paragangliomas have been described in the Gastrointestinal System, the majority of which were associated with the duodenum
A very select few were described to arise from the mesentery [2]. Given their catecholamine secreting properties, paragangliomas have the potential to present as a mass with paroxystic symptoms of palpitations, pallor, tremor, headache and diaphoresis as well as hypertension [3]

Summary

Background

With an annual incidence estimated at 1/100,000, paragangliomas represent ten percent of catecholamine secreting tumors. A very select few were described to arise from the mesentery [2] Given their catecholamine secreting properties, paragangliomas have the potential to present as a mass with paroxystic symptoms of palpitations, pallor, tremor, headache and diaphoresis as well as hypertension [3]. This is only the case in 25% of the paragangliomas. The ultrasound, which revealed an asymptomatic hypoechogenous polylobulated solid mass in the right supraumbilical territory, was followed up and confirmed with a CT scan (Figure 1). The patient has been followed for almost a year and a follow up abdominal scan was conducted, all indicating the patient was free from any signs of recurrence including the palpitations and diaphoresis

Discussion

Findings

Conclusion

Young WF Jr