Malignant metastatic steroid cell tumor NOS: A rare presentation of a subtype of sex cord stromal tumor

Abstract

Steroid cell tumors – not otherwise specified (NOS) – are rare sex cord stromal tumors that lack characteristic histology, are benign, and usually present with androgenic manifestations. Metastatic malignant steroid cell tumors pose treatment challenges due to their chemoresistance nature. This is a case report of a metastatic steroid cell tumor – NOS with extensive peritoneal disease.