Lymphatic-Venous Malformation Presenting as a Mediastinal Mass in a 6-Year-Old Boy

Abstract

Among the slow-flow vascular malformations in children, lymphatic malformation (LM; formerly known as lymphangioma) typically develops in the neck (75‒90%), with the posterior triangle being the most commonly affected site (1,2). Ninety percent of the entity is detected in children younger than 2 years (2). LM tends to behave like lymphatic-venous malformation (LVM; formerly, lymphangiohemangioma), but these two entities are clinically indistinguishable (3,4). This article describes a rare case of LVM, presenting as a new-onset, cervical mass extending to the mediastinum in a school-aged boy, that is, an unusual location and age for the malformation.