Lymphangioma circumscriptum of the vulva: a rare case report

Abstract

Lymphangioma circumscriptum (LC) is a rarely seen benign disease that involves deep dermal and subcutaneous lymphatic channels. It is seen as a group of lesions in the shape of thin-walled translucent saccules resembling frog eggs. Although the most frequently seen form of cutaneous lymphangioma is seen in the infantile period, it may occur at any age. The most common locations of these lesions are the proximal parts of extremities that contain a rich lymphatic network such as axilla, shoulder, inguinal region, and perineum. Vulvar involvement is quite rare and usually develops secondary to a radical hysterectomy, pelvic lymphadenectomy, radiotherapy, and Crohn's disease. Here, an extraordinary case of LS with an obscure cause is presented.