Lower limb giant plexiform neurofibroma: preoperative evaluation and surgical planning

Abstract

Few cases of lower limb giant plexiform neurofibroma have been reported in literature and there are no available guidelines for defining its preoperative evaluation and surgical approach . Lower limb giant plexiform neurofibroma is a rare condition that requires clinical and radiological preoperative evaluation, mainly with MRI. Surgery is the only treatment with no preoperative trans-arterial embolization or vessel ligation. Early excision of superficial lesions may prevent further progression.