Long-Term Follow-Up of Congenital Aniridia-A Case Report

Abstract

Purpose: To report the clinical course and the surgical outcomes of a patient of congenital hereditary aniridia. Results: A 27-year-old male with a history of bilateral congenital aniridia and cataract had undergone cataract extraction on his right eye at the age of 4. He suffered from blurred vision and photophobia of both eyes since childhood. On examination, the best corrected visual acuity (BCVA) was 6/20 and the intraocular pressure (IOP) was 26 mmHg in the right eye. Nystagmus was noted. Slit lamp biomicroscopy showed incomplete aniridia in both eyes, aphakia with fibrotic capsular bag, focal peripheral anterior synechiae and prolapsed vitreous in the right eye. Fundus examination revealed bilateral foveal hypoplasia. We perfomed sutured-intraocular lens (IOL) implantation, trabeculectomy, and anterior vitrectomy on his right eye. The BCVA preserved at 6/20 with well-controlled IOP at one year's follow-up. Conclusion: Congenital aniridia is rare and causes a variety of ocular complications. There are various surgical managements at present. We chose sutured-IOL and trabeculectomy for this patient and got satisfactory outcomes.