Localized Pigmented Villonodular Synovitis in a Child: About a Case

Abstract

Pigmented Villonodular synovitis (PVNS) is a rare benign proliferative condition affecting synovial membranes of joints; it occurs in two forms, localized (LPVNS) and diffuse (DPVNS). We report a case of a 12 years old with LPVNS, confirmed on surgical biopsy. The patient underwent a surgical synovectomy, with good evolution after 1 year follow-up. PVNS is most common in early to middle age, It still exceptional in children. Clinically, its symptology remains aspecefic. This is often a cause of delay in diagnosis. Magnetic resonance imaging (MRI) is the exam of choice. Only a synovial biopsy with histological study confirms the diagnosis; the treatment typically involves surgery: synovectomy, with a risk of recurrence.