Abstract
Left ventricular noncompaction (LVNC) is a rare form of cardiomyopathy characterized by prominent left ventricular (LV) trabeculae, deep intertrabecular recesses, and the thin compacted layer. The disease is potentially associated with sudden cardiac death due to LV dysfunction and ventricular arrhythmias. The presence of accessory pathway and Wolff-Parkinson-White syndrome is particularly rare in adults. Here we describe the rare association of LVNC and ventricular pre-excitation in an 18-year-old female with neonatal hypoxic brain injury. Keywords: Wolff-Parkinson-White syndrome; pre-excitation syndromes; isolated noncompaction of the ventricular myocardium
Highlights
Left ventricular noncompaction (LVNC) is a rare form of cardiomyopathy characterized by prominent left ventricular (LV) trabeculae, deep intertrabecular recesses, and the thin compacted layer
LVNC occurs in infants (0.81 cases/100,000 per year), children (0.12 cases/100,000 per year) and adults[1]
The disease is defined by three markers: prominent LV trabeculae, deep intertrabecular recesses, and a thin C layer[1]
Summary
Left ventricular noncompaction (LVNC) is a rare form of cardiomyopathy characterized by prominent left ventricular (LV) trabeculae, deep intertrabecular recesses, and the thin compacted layer. Left ventricular noncompaction (LVNC) is a rare form of cardiomyopathy characterized by prominent left ventricular (LV) trabeculae, deep intertrabecular recesses, and the thin compacted (C) layer[1]. The disease is potentially associated with sudden cardiac death (SCD) due to LV dysfunction and ventricular arrhythmias. The presence of accessory pathway and Wolff-Parkinson-White (WPW) syndrome is rare in adults[2,3].
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