Abstract
Proximal interruption of the unilateral pulmonary artery is a rare congenital anomaly, which is often associated with other cardiovascular abnormalities. It is usually diagnosed in children but rarely discovered in adulthood as an isolated phenomenon, occurring more frequently on the right side and is often associated with a contralateral aortic arch. We are presenting a rare case of a sixty year old male who was diagnosed with left lung hypoplasia due to proximal interruption of left pulmonary artery with left sided aortic arch without any associated cardiovascular anomalies. DOI: http://dx.doi.org/10.3329/bjms.v12i4.13689 Bangladesh Journal of Medical Science Vol. 12 No. 04 October 13 Page 462-466
Highlights
Unilateral pulmonary artery agenesis (UPAA) is a rare entity with an incidence of about one in 200,000 individuals[1] and it is often associated with other developmental anomalies of cardiovascular system
We hereby describe a case of left sided pulmonary artery agenesis with hypoplasia of left lung without any cardiological abnormality, which was diagnosed late in his life and had a samesided aortic arch
Case Presentation A thin built sixty year old male patient presented to our pulmonary medicine OPD with complaints of occasional left sided chest pain over last one year
Summary
Unilateral pulmonary artery agenesis (UPAA) is a rare entity with an incidence of about one in 200,000 individuals[1] and it is often associated with other developmental anomalies of cardiovascular system. Several hypotheses like chromosomal anomaly, vitamin A deficiency, intrauterine infection and environmental factors have been proposed[3], no definite aetiology has been detected till Diagnosis of this condition is usually made during childhood, but it may be delayed till late adulthood, especially in asymptomatic patients. Case Presentation A thin built sixty year old male patient presented to our pulmonary medicine OPD with complaints of occasional left sided chest pain over last one year. He had no history of breathlessness, palpitation, cough, fever or haemoptysis.
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