Left pulmonary artery agenesis : fortuitous discovery in adulthood

Abstract

E lies such as tetralogy of Fallot, septal defects, coarctation of the aorta, subvalvular aortic stenosis, transposition of the great arteries, pulmonary stenosis. These are in most cases diagnosed and treated during the patient’s first year of life [1]. On the contrary, isolated UPAA may remain asymptomatic in 30% of cases [2] such as in the current case, or has a benign clinical course osition of the great vessels was associated. Unilateral ulmonary Artery Agenesis (UPAA) is a rare congental anomaly, with less than 200 cases reported in the iterature. UPAA results from a failure of connection etween the sixth aortic arch and the pulmonary trunk. It smost frequently accompaniedby cardiovascular anomaleading to a tardive diagnosis in adulthood. Severe pulmonary hypertension and congestive heart failure are to be feared, which may occur in 40% of cases [2]. Main symptomsarenot specific, including recurrent pulmonary infections, dyspnea or limited exercise tolerance and haemoptysis [3].