Abstract
BackgroundPrimary cardiac schwannoma in the left atrium and schwannomatosis are rare diseases.Case presentationWe report the case of a 46-year-old asymptomatic man who had tumor resection for parapharyngeal schwannoma at another institute 1 year ago. He was presented to our hospital for further evaluation of an abnormal cardiac shadow that was found incidentally. Computed tomography and transesophageal echocardiography revealed a cardiac tumor originating from the posterior wall of the left atrium, an atrial septal defect, and two other mediastinal tumors. The cardiac mass was completely excised with normal margins of the surrounding atrial wall. The post-resection defect and atrial septal defect were repaired using bovine pericardium. Pathological findings were compatible with benign schwannoma, and a diagnosis of schwannomatosis was made based on his medical history.ConclusionPrimary cardiac schwannoma is an exceedingly rare tumor, and the incidence in schwannomatosis has not been reported in the literature.
Highlights
Primary cardiac schwannoma in the left atrium and schwannomatosis are rare diseases.Case presentation: We report the case of a 46-year-old asymptomatic man who had tumor resection for parapharyngeal schwannoma at another institute 1 year ago
Primary cardiac schwannoma is an exceedingly rare tumor, and the incidence in schwannomatosis has not been reported in the literature
We report a case of schwannomatosis with cardiac schwannoma in the left atrium, and two other mediastinal tumors in a patient with previous resection of a parapharyngeal schwannoma
Summary
Cardiac schwannoma is one of the rarest benign cardiac neoplasms [1]. schwannomatosis is an extremely rare genetic disorder closely related to neurofibromatosis. We report a case of schwannomatosis with cardiac schwannoma in the left atrium, and two other mediastinal tumors in a patient with previous resection of a parapharyngeal schwannoma. Case presentation A 46-year-old asymptomatic man presented to our hospital for follow-up of an abnormal cardiac shadow found on chest X-ray during a medical check-up. He was found to have a benign tumor in the parapharyngeal space 6 years ago. The patient underwent transesophageal echocardiography (TEE), which revealed that the mass was a cardiac tumor originating from the posterior wall of the left atrium (LA) without a stalk (Fig. 2). One year after the cardiac tumor resection, no findings suggestive of recurrence of cardiac tumor were noted and followup tests, such that TEE and CT showed no significant growth of the two remnant mediastinal tumors or residual shunt
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