Kaposiform haemangioendothelioma: A radiological dilemma

Abstract

Kaposiform haemangioendothelioma (KHE) is a rare, locally aggressive vascular tumours diagnosed in infancy or early childhood. KHE has a worse prognosis than infantile or congenital haemangioma due to its infiltrative nature and risk of developing Kasabach-Merritt Syndrome (KMS). This case report is about a 4-month-old girl who presented with progressive left neck swelling. She was diagnosed with KHE and thrombocytopenia suggestive of Kasabach-Merritt Syndrome (KMS). We describe the imaging appearance of KHE on ultrasound and magnetic resonance imaging. We also highlight the importance of integrating patient’s clinical history with the physical, laboratory and imaging findings for early diagnosis to prevent disease-related life-threatening complications.