Abstract
The histiocytoses are a heterogenous group of diseases that are characterized by the accumulation of reactive or neoplastic histiocytes in various tissues. Juvenile Xanthogranuloma is a member of the non-Langerhans cell group of histiocytic proliferative disorders. This present case report describes a juvenile xanthogranuloma in a twenty-month old male baby.Nepal Journal of Dermatology, Venereology & Leprology, Vol.14(1) 2016, pp.56-58
Highlights
Juvenile xanthogranuloma (JXG) is a rare disorder, which belongs to the broad group of non Langerhans cell his ocytosis
JXG represents an accumula on of his ocytes lacking Birbeck granules which can be differen ated from Langerhans cells by specific staining techniques.[3]
Skin biopsy was taken from a papule in right cheek which showed foamy macrophages in aggregates intermingled with lymphocytes, touton’s giant cells were noted sugges ve of Juvenile Xanthogranuloma
Summary
Juvenile xanthogranuloma (JXG) is a rare disorder, which belongs to the broad group of non Langerhans cell his ocytosis. The non-LCH are generally benign prolifera ve disorders but may have a systemic component as a major part of the disease.[1] Juvenile xanthogranulomas are benign tumours of his ocy c cells that occur predominantly in infancy and early childhood and spontaneously regress.[2] The classic presenta on is that of successive erup ons in the head, neck, and upper trunk of ini ally red papules or nodules which later become yellow and brown fla ened plaques or macules.
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