Juvenile Angiofibroma Occurring in an Unusual Site: Report of a Case

Artur Bartosz Niedzielski

doi:10.4172/2161-0665.1000235

Abstract

Extra Nosopharyngeal Angiofibromas (ENA) is a tumor of fibrotic and angiovascular consistency which are localized outside the nasopharyngx (i.e. nasal septum). The clinical characteristic of ENA and JNA (juvenile angiofiborma) is not conclusive and the diagnosis of the ENA is problematic. The nine year old girl was administered to the Children Otolaryngology Clinic. The histopathological examination proved that the removed mass was angiofibroma. According to literature and our clinical experience it is important to be aware of the atypical localization of the juvenile angiofibromas. According to literature only about 15 cases of the similar case were reported.

Highlights

Angiofibromas are rare, benign tumors of the vascular and fibrous connective tissue composure
The nasal septum is a very rare site of extra nasopharyngeal angiofibroma with only two cases reported in the medical literature [6]
The computed tomography (Figure 7) and the magnetic resonance are the mainstay in the case of Extra Nosopharyngeal Angiofibromas (ENA) because the biopsy is contraindicated

Summary

Introduction

Angiofibromas are rare, benign tumors of the vascular and fibrous connective tissue composure. The lesion is benign it can present local malignancy. In advanced cases it can extend intracranially. The incidence of the JNA is less than 0.5% of tumors arising in the head and neck [3]. In USA this lesion is the most frequent head and neck tumor of the adolescence with 1 new case per 5000 to 50000 patients referred to otolaryngologist [4]. Glad and colleagues reported an incidence of JNA in Denmark of 0.4 cases per million inhabitants per year. Symptoms of the JNA depend on tumor size, localization andextend. The material was send to the histopathological examination This tumor is composed of two basic components: fibrocallagenousstroma and many vascular channels. Mitotic figures are rare and usually no cytologicatypia is seen (Figures 1-7)

Background and Case Presentation

Findings

Discussion

Conclusion