Junctional Epidermolysis Bullosa of the Larynx

Abstract

To the Editor.— The article by Kenna et al (Pediatrics 1986;78:172-174) points out the complication of respiratory compromise secondary to laryngeal involvement in junctional epidermolysis bullosa. Junctional epidermolysis bullosa, a mechanobullous disorder with autosomal recessive inheritance, has been associated with not only skin lesions but gastrointestinal, respiratory tract, and genitourinary tract abnormalities as well.1 The figure that was presented in the article incorrectly showed a split in the upper layers of the epidermis inconsistent with junctional epidermolysis bullosa.