Isolated Noncompaction of the Myocardium

Abstract

To the Editor: Isolated noncompaction of the ventricular myocardium is a rare congenital disorder. We have reported elsewhere that the incidence of this unique cardiomyopathy is 0.05 percent in adults.1 In the report of the 1995 World Health Organization–International Society and Federation of Cardiology task force on the definition and classification of cardiomyopathies, noncompacted myocardium has been categorized as unclassified cardiomyopathy.2 Noncompaction refers to the arrest of compaction of the loosely interwoven meshwork of myocardial fibers during embryogenesis.3 The loose meshwork becomes more compact toward the epicardial surface and condenses to a compact wall, and the intertrabecular recesses communicating with . . .