Abstract
Unilateral pulmonary artery agenesis without any cardiovascular malformation is a rare anomaly. We present the imaging findings of a patient who was diagnosed as isolated left pulmonary artery agenesis. A 27-year-old female patient was admitted to our hospital due to dyspnea during exercise for five years. Chest X-ray revealed minimally small left pulmonary hilum and left lung. She was admitted to our clinic with the suspicion of pulmonary artery pathology. Absent perfusion of the left lung with normal ventilation was visualized on scintigraphy. MDCT angiography of pulmonary arteries showed absent left main pulmonary artery with systemic collaterals around left hemithorax. Pulmonary artery agenesis can be asymptomatic and isolated until adulthood. Both scintigraphy and CT angiography images of pulmonary artery agenesis of a patient are rare in the literature. Pulmonary ventilation-perfusion scintigraphy can be used not only for pulmonary embolism but also pathologies involving pulmonary artery and its branches. Conflict of interest:None declared.
Highlights
Isolated unilateral absence of pulmonary artery is a rare congenital malformation
We present the chest radiography, ventilation-perfusion scintigraphy and computed tomography (CT) angiography images of this rare malformation
Unilateral pulmonary artery agenesis and hypoplasia should be especially suspected in case of small hemithorax and ipsilateral small pulmonary hilum on chest radiograph [7]
Summary
Tansel Ansal Balcı, Zehra Pınar Koç, Gamze Kırkıl 2, Ahmet Kürşad Poyraz3 1Fırat University Faculty of Medicine Department of Nuclear Medicine, Elazığ, Turkey 2Fırat University Faculty of Medicine, Department of Pulmonary Disease, Elazığ, Turkey 3Fırat University Faculty of Medicine, Department of Radiology, Elazığ, Turkey
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